ANSWER: Marfan
syndrome with dilatation of the aortic root and ascending thoracic aorta,
and aortic regurgitation.
.
Figures 1 and 2. Frontal and
lateral chest radiographs show cardiomegaly and dilatation
of the ascending thoracic aorta.
Note obliteration of the retrosternal clear space by the
dilated ascending thoracic aorta.
Figures 3 and 4. Coronal and oblique sagittal MRI
with T1-weighted spin echo technique show huge
dilatation of the aortic root and the ascending thoracic
aorta. Note the dilated left ventricle.
Figure 5. Cine MRI shows regurgitation of blood from
the aortic root into
the left ventricle (note signal void in the left ventricle)