Congenital cystic adenomatoid malformation is caused by anomalous fetal
development of terminal respiratory structures [1]. This lesion is usually
unilateral, involving all or part of a lung [2]. It has both cystic and
solid tissue. It can be classified on the basis of clinical, radiographic,
and histological features [1,3]. Type I has cysts of varying sizes with
at least one cyst with a diameter of more than 2 cm. Type II has smaller
cysts of more uniform size with diameter of 2 cm or less. Type III has
microcysts, which appear solid. Most patients with this condition present
with respiratory distress in the neonatal period or shortly thereafter.
However, those with small lesions may present later with symptoms of pulmonary
infection [4].
The radiographic appearance of congenital cystic adenomatoid malformation
depends on type, age of the patient, and presence of complications such
as infection [1-3]. Immediately after birth it appears as a water density
mass, which shifts the mediastinum toward the opposite side. A short
time later fluid leaves the mass, which then appears reticulated or bubbly.
Type I lesions have one or more dominant cysts with adjacent smaller cysts
and solid elements. Type II lesions have smaller, more evenly sized cysts.
Type III lesions appear as a solid mass.
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